Moebius sendromu: ‹ki olgu sunumu Moebius syndrome: Report of two cases
نویسندگان
چکیده
Yaz›flma adresi: Dr. Semra Kurul, Dokuz Eylül Üniversitesi T›p Fakültesi, Çocuk Sa¤l›¤› ve Hastal›klar› Anabilim Dal›, Çocuk Nörolojisi Bilim Dal›, 35340 ‹nciralt›/‹zmir Özet Moebius sendromu konjenital fasyal sinir ve s›kl›kla alt›nc› sinir olmak üzere di¤er kranyal sinirlerin paralizisi ve/veya kas -iskelet sistemi anomalileri ile giden bir hastal›kt›r. Sendromun patogenezi aç›k de¤ildir, ancak en önemli hipotez prenatal beyin sap› iskemisidir. Bu yaz›da Moebius sendromu tan›s› alm›fl iki olgu sunulmufl ve hastal›¤›n etiyoloji ve ay›r›c› tan›s› tart›fl›lm›flt›r. Anahtar kelimeler: Moebius sendromu, konjenital fasyal palsi
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